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Rabbit Anti-EXPH5/BF594 Conjugated antibody (bs-2834R-BF594)
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說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-2834R-BF594
英文名稱 Rabbit Anti-EXPH5/BF594 Conjugated antibody
中文名稱 BF594標記的EXPH5蛋白抗體
別    名 DKFZp586F1223; DKFZp781H0795; Exophilin 5; Exophilin5; KIAA0624; MGC133291; EXPH5_HUMAN; MGC134967; SLAC2-B; SLAC2B; slp homolog lacking C2 domains b; synaptotagmin-like homologue lacking C2 domains b; synaptotagmin-like protein homolog lacking C2 domains b.  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  信號轉導  G蛋白信號  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 222kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human EXPH5
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
May act as Rab effector protein and play a role in vesicle trafficking.

Function:
May act as Rab effector protein and play a role in vesicle trafficking.

Subunit:
Interacts with RAB27A (By similarity).

Tissue Specificity:
Expressed in keratinocytes.

DISEASE:
Epidermolysis bullosa, non-specific, autosomal recessive (EBNS) [MIM:615028]: A skin disease characterized by blistering of skin and mucosae, following minimal pressure or trauma. Various clinical types with different severity are recognized, ranging from severe mutilating forms to mild forms with limited and localized scarring, and less frequent extracutaneous manifestations. EBNS clinical features mainly comprise trauma-induced scale crusts and intermittent skin blistering. Some of the crusted areas are hemorrhagic and accompanied by occasional bruising. Most lesions clear over several weeks to leave slightly atrophic scars and moderate post-inflammatory hyperpigmentation. Note=The disease is caused by mutations affecting the gene represented in this entry.

Similarity:
Contains 1 RabBD (Rab-binding) domain.

Database links:

Entrez Gene: 23086 Human

Omim: 612878 Human

SwissProt: Q8NEV8 Human



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
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